Rosai-dorfman disease in pregnancy with rare presentations – A case report
نویسندگان
چکیده
Rosai-Dorfman disease (RDD) also known as sinus histiocytosis with massive lymphadenopathy is a rare disorder of histiocytes characterized histologically by intracellular engulfment lymphocytes. It may occur in any age group, but most commonly seen children and young adults. painless, bilateral cervical lymphadenopathy. In approximately one-third patients it can variety extranodal sites where have abundant plasma cells sclerosis. We present case RDD pregnant women who presented unilateral lymph node features showing increase sclerosis sites.
منابع مشابه
Rosai-Dorfman Disease: A Case Report and Literature Review
Rosai-Dorfman disease or sinus histiocytosis with massive lymphadenopathy is a rare disorder that typically manifests as lymphadenopathy and systemic symptoms whose etiology remains poorly elucidated. The diagnosis is based on immunohistochemistry. Its treatment is poorly defined but the prognosis is usually favorable. Here we report a 14 year old boy who presented with massive bilateral cervi...
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ژورنال
عنوان ژورنال: Journal of diagnostic pathology and oncology
سال: 2023
ISSN: ['2456-6284', '2581-3706', '2581-3714']
DOI: https://doi.org/10.18231/j.jdpo.2023.023